Department of radiology, Faculty of medicine,
Case 9 :
An 8 year old girl falled from a tree. This is her chest radiograph. What is the diagnosis?
Small (hypoplastic) right lung and ipsilateral anomalous pulmonary venous drainage to IVC - with Turkish sword (scimitar) appearance of the anomalous vein- seen from chest radiograph are diagnostic for scimitar syndrome (pulmonary venolobar syndrome).
Forty percents of patients are asymptomatic, while the other 60% develop dyspnea on exertion in the 2nd or 3rd decade of life, depending to extension of the left to right shunt.
When the diagnosis is suspected from chest X-ray, further investigation with CTA or MRA is recommended.